Rapunzel syndrome presenting as acute pancreatitis, hypoproteinaemia and subsequent distal intestinal obstruction

Mckusick-Kaufman Syndrome Presenting as Acute Intestinal Obstruction

Hydrometrocolpos and polydactyly have been associated with many syndromes and can present at any age. Rarely does hydrometrocolpos present as neonatal intestinal obstruction. We report two cases of McKusick-Kaufman syndrome presenting with intestinal obstruction. In both cases, intestinal obstruction got relieved after a cutaneous vaginostomy.

Distal intestinal obstruction syndrome.

A 31-year-old woman with cystic fibrosis (CF) presents with a rightsided obstructive pyeloureteral junction stone complicated by urosepsis. Following an emergency treatment with ureteral stent placement, she is transferred to the intensive care unit for symptoms of septic shock and hemodynamic instability. Her clinical history reveals an exocrine pancreatic insufficiency and bilateral lung tran...

Neonatal Currarino's syndrome presenting as intestinal obstruction.

Laparoscopy in Afferent Loop Obstruction Presenting as Acute Pancreatitis

BACKGROUND We describe an afferent loop obstruction caused by an adhesion band in a case of distal gastrectomy with Roux-en-Y end-to-side jejunal anastomosis for cancer. METHODS An initial clinical presentation of acute pancreatitis was ruled out by a computed tomography scan, which revealed intestinal obstruction; it was then confirmed on laparoscopy. Definitive treatment was laparoscopic ad...

Splenic Torsion in a Wandering Spleen Presenting As Intestinal Obstruction

SUMMARY The -presented patient is a 4 year old boy who is a known case of Niemannpick disease. He presented with restlessness, anorexia, Vomiting and constipation. On the physical exam the cbdomen was distended and a large and a large and mobile mass in right lower quadrant was palpated. Plain abdominal X-Ray showed air-fluid levels. The patient underwent an emergent operation. The splenic ped...